Perianal eccrine adenocarcinoma

BACKGROUND Eccrine carcinoma is a quite rare malignant tumor that typically arises from a normal sweat gland and that features a rather high recurrence rate subsequent to simple excision. Given its rather poor response to adjuvant therapy, wide excision of the lesion with tumor-free margins may offer a reasonable chance for long-term control of this neoplasm. CASE PRESENTATION Herein, we report on an unusual case of perianal eccrine carcinoma, initially presenting as a perianal abscess. CONCLUSION Even though eccrine carcinomas would appear to be rare, when dealing with recurrent skin tumors or recurrent perianal fistulas, the possibility of eccrine carcinoma should be considered by consulting clinicians.