primitive neuroectodermal tumor of the kidney in a 22-year-old male: a rare entity

primitive neuroectodermal tumors of the kidney are rare tumors representing about 1% of all sarcomas. extraskeletal primitive neuroectodermal tumors may be found in the genitourinary tract, the testes, ovaries, uterus, or pancreas. renal primitive neuroec- todermal tumors are frequently aggressive and almost 30% of all newly diagnosed cases present with distant metastases. surgical intervention, intensive chemotherapeutic drugs and radiation therapy are the best choices for management. we discuss the case of a 22-year-old male who presented with a left renal mass. he underwent nephrectomy followed by histopathological examination. microscopic and immunohistochemical examination revealed a primitive neuroectodermal tumor.