periodontal manifestations and unusual radiographic features in a patient with sturge-weber syndrome: a case report
نویسندگان
چکیده
the sturge-weber syndrome or encephalotrigeminal angiomatosis is a rare neurological and congenital disorder with a frequency of 1 in 50,000 births. this syndrome is a nonhereditary developmental condition and is characterized by the presence of congenital capillary malformation and a hamartomatous vascular proliferation involving the face (port-wine stain or facial birthmark), sometimes skull and the tissues of brain, jaws, oral soft and hard tissues and rarely other body organs. seizures, mental retardation, and cortical calcification (tram-tracks) and congenital glaucoma may be seen in this syndrome. we report here a 40-year-old female with sturge-weber syndrome associated with bilateral cutaneous capillary malformation on her face, neck, hands and feet and also gingival enlargement.
منابع مشابه
Management of patient with Sturge-Weber syndrome: a case report
INTRODUCTION Sturge-Weber syndrome sometimes referred to as encephalotrigeminal angiomatosis, is a rare congenital neurological and skin disorder. CASE PRESENTATION This is case report of a 18-year-old mentally disabled boy, with long-standing seizures, with a port-wine nevi on the left side of the face along the distribution of trigeminal nerve. Interictal encephalogram showed bilateral slow...
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Sturge-Weber angiomatosis is a rare, nonhereditary developmental condition characterized by a hamartomatous vascular proliferation involving the tissues of brain and face. A report of a case with facial port wine stains, gingival overgrowth, and dilated ocular vessels is described.
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Sturge Weber Syndrome or encephalo-trigeminal angiomatosis is non-hereditary, congenital and rare disorder of unknown aetiology. It is characterised by vascular malformation with capillary venous angiomas involving face, eye and leptomeninges resulting in neurological and orbital manifestations. A case of 23 years old female presented with history of tonic-clonic convulsions, evidence of Port w...
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Sturge-Weber syndrome (SSW) is a congenital neurocutaneous disorder, which presents a port wine vascular malformation that covers the territory of the trigeminal nerve, neurological manifestations (ipsilateral leptomeningeal involvement, seizures and mental retardation) and ophthalmic signs (choroidal vascular malformation, glaucoma). There is no evidence to indicate that this is an inherited d...
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عنوان ژورنال:
journal of periodontology and implant dentistryجلد ۶، شماره ۱، صفحات ۲۸-۰
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