dopa responsive dystonia: a case report

نویسندگان

mohammad ghofrani from the department of pediatric neurology, mofid children's hospital, shahid beheshti university of medical sciences, tehran, i.r. iran

hassan tonekaboni

چکیده

dopa responsive dystonia (drd) is a dystonic syndrome of childhood, usually affecting gait and subsequently developing into parkinsonism with a dramatic therapeutic response to levodopa. at the best of our recollection this is the first case in iranian medical literature of a 13 year old boy, affected by this interesting, rare and treatable disease which can be easily diagnosed if clinicians have a high index of suspicion. we also have a brief discussion on the pathophysiology of drd.

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DOPA RESPONSIVE DYSTONIA: A CASE REPORT

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عنوان ژورنال:
medical journal of islamic republic of iran

جلد ۱۳، شماره ۳، صفحات ۲۳۵-۲۳۶

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