familial dysautonomia, report of 3 cases from iran and a discussion about their general and anaesthesia care
نویسندگان
چکیده
background: familial dysautonomia (fd) is a rare hereditary syndrome which is an autosomal recessive trait that typically affects jewish children. important signs and symptoms of the disorder include; diminished pain perception, absence of overflow tears, hypotonia, fainting cardiac arrhythmias and autonomic crisis. cases report : in this article we reported 3 cases of fd syndrome which had presented for surgical operation followed by a discussion about general care of these patients as well as anesthesia considerations.
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عنوان ژورنال:
novelty in biomedicineجلد ۳، شماره ۲، صفحات ۹۴-۹۸
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