familial dysautonomia, report of 3 cases from iran and a discussion about their general and anaesthesia care

نویسندگان

badiozaman radpay department of anesthesiology critical care and pain management, lung transplantation research center, national research institute of tuberculosis and lung disease, tehran, iran

mahtab poor zamany nejat kermany department of anesthesiology, labbafinejad medical center, shahid beheshti university of medical sciences, tehran, iran

ali asghar halimi-asl department of pediatrics, shohada tajrish medical center, shahid beheshti university of medical sciences, tehran, iran

چکیده

background: familial dysautonomia (fd) is a rare hereditary syndrome which is an autosomal recessive trait that typically affects jewish children. important signs and symptoms of the disorder include; diminished pain perception, absence of overflow tears, hypotonia, fainting cardiac arrhythmias and autonomic crisis. cases report : in this article we reported 3 cases of fd syndrome which had presented for surgical operation followed by a discussion about general care of these patients as well as anesthesia considerations.

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عنوان ژورنال:
novelty in biomedicine

جلد ۳، شماره ۲، صفحات ۹۴-۹۸

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