pericardial effusion in langerhans cell histiocytosis: a case report
نویسندگان
چکیده
conclusions pericardial effusion was a rare finding in this case of langerhans cell histiocytosis. pericardial effusion in langerhans cell histiocytosis, which is an unusual presentation, should be considered when the patient experiences respiratory distress. introduction langerhans cell histiocytosis (lch) is a proliferative disorder of histiocytes in multiple organs. langerhans cell histiocytosis involves bones, skin, lung and other organs. case presentation this study describes a seven-month-old iranian girl who presented with skin rash and cervical lymphadenopathy. langerhans cell histiocytosis was suspected when it was associated with anemia, splenomegaly and lytic bone lesions. a skin biopsy confirmed the diagnosis of langerhans cell histiocytosis. during hospitalization, the patient looked ill with respiratory distress. a chest x-ray showed a ground glass view, and echocardiography showed moderate pericardial effusion.
منابع مشابه
Pericardial Effusion in Langerhans Cell Histiocytosis: A Case Report
INTRODUCTION Langerhans cell histiocytosis (LCH) is a proliferative disorder of histiocytes in multiple organs. Langerhans cell histiocytosis involves bones, skin, lung and other organs. CASE PRESENTATION This study describes a seven-month-old Iranian girl who presented with skin rash and cervical lymphadenopathy. Langerhans cell histiocytosis was suspected when it was associated with anemia,...
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عنوان ژورنال:
iranian red crescent medical journalجلد ۱۸، شماره ۶، صفحات ۰-۰
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