Systemic mastocytosis: Case report with literature review
نویسندگان
چکیده
منابع مشابه
Systemic mastocytosis with skeletal involvement: a case report and review of the literature.
Systemic Mastocytosis (SM) comprises a heterogeneous group of disorders of mast cell proliferation. Infiltration, including skin and bone, of multiple mast cells may occur as cutaneous and systemic variants. A rare form of osteoporosis has been also described as expression of the skeletal involvement. Here, we describe a case of a 57-years-old woman with SM and, according to the clinical diagno...
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Systemic mastocytosis is characterized by abnormal growth and accumulation of mast cells in various organs. Gastrointestinal (GI) symptoms are common disease manifestations in this disease and can significantly impair the quality of life. Signs of GI systemic mastocytosis include steatorrhea, malabsorption, hepatomegaly, splenomegaly, portal hypertension, and ascites. Acute appendicitis as a pr...
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Introduction: Anaphylaxis is defined as “a serious, life-threatening generalized or systemic hypersensitivity reaction” and “a serious allergic reaction that is rapid in onset and might cause death”. The determination of different mast cells (MC) mediators, such as serum and/or plasma histamine and tryptase, is proposed for the diagnosis of anaphylaxis. There are differences in the clinical pre...
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CONTEXT Systemic mastocytosis is defined as a clonal disorder of mast cells and their precursor cells and is currently classified as a myeloproliferative neoplasm. Its clinical course has a wide spectrum, ranging from indolent disease, with normal life expectancy, to highly aggressive disease, associated with multisystemic involvement and poor overall survival. The aim of this study was to repo...
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Mastocytosis is a rare heterogeneous group of diseases with multi-organ involvement. Gastrointestinal (GI) tract infiltration by neoplastic mast cell is uncommon in systemic mastocytosis. In our literature review, there are only 11 published mastocytosis reports including 42 cases of biopsy confirmed direct colon involvement. We report here a rare case of focal mastocytosis in the rectum withou...
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ژورنال
عنوان ژورنال: Srpski arhiv za celokupno lekarstvo
سال: 2012
ISSN: 0370-8179,2406-0895
DOI: 10.2298/sarh1202100m