Sturge Weber Syndrome- A Rare Congenital Neuro-cutaneous Disease
نویسندگان
چکیده
منابع مشابه
The cutaneous angioma of Sturge-Weber syndrome.
A 16-month-old male presented with focal motor seizures with secondary generalization. On physical exam, a bilateral facial cutaneous angioma, sharply demarcated by the distribution of the ophthalmic and maxillary branches of the trigeminal nerve, was noted (Figure 1). Magnetic resonance imaging (MRI) demonstrated calcification and atrophy of the right frontal lobe as well as an associated pial...
متن کاملCongenital Glaucoma from Sturge-Weber Syndrome: A Modified Surgical Approach
Sturge-Weber syndrome (SWS) is a rare congenital neurocutaneous disorder that causes congenital glaucoma. Previous experiences have shown that drainage procedures are often required to control associated glaucoma. The conventional surgical approach in trabeculectomy carries a significant risk of intraoperative expulsive hemorrhage. Here, we describe a modified approach of the conventional trabe...
متن کاملAngiodysplastic Sturge Weber syndrome.
Accepted 19 November 2017 DesCripTion A 3-year-old boy presented with global developmental delay, abnormal craniofacial growth and left focal seizures since infancy. He was the first child of a non-consanguineous couple with unremarkable perinatal period. Family history was non-contributory. On examination, he had macrocephaly (head circumference 55 cm, >3 z-score), extensive port-wine stain di...
متن کاملBilateral Sturge Weber syndrome- a rare case report.
BACKGROUND Sturge-Weber syndrome is a rare congenital neuro- oculo- cutaneous disorder. OBJECTIVE To report a very rare unusual case of bilateral manifestation of Sturge Weber syndrome. CASE We report an unusual case of a 17-year-old female with advanced stage of bilateral glaucoma associated with facial nevus extending to the other half of the face as well and bilateral intracranial calcif...
متن کاملSturge-Weber Syndrome
Sturge-Weber syndrome (SWS) is a neurocutaneous syndrome, characterized by the association of facial port-wine hemangiomas in the trigeminal nerve distribution area, with vascular malformation(s) of the brain (leptomeningeal angioma) with or without glaucoma. Herein, we reported Sturge-Weber syndrome in a 50-year-old man, who presented port-wine hemangiomas and epilepsy. In this case, the patie...
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ژورنال
عنوان ژورنال: Update Dental College Journal
سال: 2016
ISSN: 2307-3160,2226-8715
DOI: 10.3329/updcj.v5i2.27275