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Síndrome de Cogan Reese Cogan Reese syndrome
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The clinical and neuroradiologic features in 22 patients with septooptic dysplasia are reviewed. The most consistent abnormality seen in 15 patients was absence of the septum pellucidum and flattening of the roofs and inferior pointing of the floors of the anterior horns of the lateral ventricles. Hypoplasia of the anterior optic pathways was seen in 10 patients and a primitive optic ventricle ...
متن کاملPeripheral retinal nonperfusion in septo-optic dysplasia (de Morsier syndrome).
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INTRODUCTION Septo-optic dysplasia (De Morsier syndrome) is defined as the association between optic nerve hypoplasia, midline central nervous system malformations and pituitary dysfunction. CASE REPORT Third child born to nonconsanguineous parents, female, adequate pre-natal medical care, cesarean term delivery due to breech presentation, Apgar score 3 at the first minute and 8 at 5 minutes,...
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ژورنال
عنوان ژورنال: Revista Medica Sinergia
سال: 2018
ISSN: 2215-5279,2215-4523
DOI: 10.31434/rms.v3i10.145