Screening for hereditary angioedema (HAE) at 13 emergency centers in Osaka, Japan
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چکیده
منابع مشابه
Screening for hereditary angioedema (HAE) at 13 emergency centers in Osaka, Japan
Hereditary angioedema (HAE) with deficiency of C1 inhibitor (C1-INH) is an autosomal-dominant disease characterized by recurrent episodes of potentially life-threatening angioedema. The objective is to study the incidence of HAE among patients who visit the emergency department.This was a 3-year prospective observational screening study involving 13 urban tertiary emergency centers in Osaka pre...
متن کاملGuideline for hereditary angioedema (HAE) 2010 by the Japanese Association for Complement Research - secondary publication.
This guideline was provided by the Japanese Association for Complement Research targeting clinicians for making an accurate diagnosis of hereditary angioedema (HAE), and for prompt treatment of the HAE patient in Japan. This is a 2010 year version and will be updated according to any pertinent medical advancements.
متن کاملDedicated call center (SOS-HAE) for hereditary angioedema attacks: study protocol for a randomised controlled trial
BACKGROUND Despite the availability of guidelines for the specific treatment of hereditary angioedema (HAE) attacks, HAE morbidity and mortality rates remain substantial. HAE attacks are a major medical issue requiring specific treatment as well as a considerable socio-economic burden. We report a protocol designed to test whether a dedicated call centre is more effective than usual practice in...
متن کاملTryptase and histamine in patients with angioedema due to C1-inhibitor deficiency (Hereditary Angioedema, HAE) and in patients with mastocytosis
Material and methods. The determinations were performed in 14 mastocytotic patients, including 6 patients with the systemic mastocytosis and 8 with urticaria pigmentosa, in 14 with innate angio-motor oedema due to C1 inhibitor deficiency, and in 10 healthy controls. Tryptase levels were determined using PhadiaUniCAP TRYPTASE reagents. Histamine concentrations were measured using HISTAMINE ELISA...
متن کاملThe hereditary angioedema burden of illness study in Europe (HAE-BOIS-Europe): background and methodology
BACKGROUND Hereditary angioedema (HAE) is a rare but serious disease marked by swelling attacks in the extremities, face, trunk, airway, or abdominal areas that can be spontaneous or the result of trauma and other triggers. It can be life-threatening due to the risk of asphyxiation. While there have been major advancements in our understanding of the immunogenetics of HAE, there are significant...
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ژورنال
عنوان ژورنال: Medicine
سال: 2017
ISSN: 0025-7974
DOI: 10.1097/md.0000000000006109