Scleroderma; hemiatrophy of face and limbs
نویسندگان
چکیده
منابع مشابه
Progressive facial hemiatrophy with localized scleroderma.
A 46-year-old woman who presented with progressive facial hemiatrophy (PFH) following localized scleroderma is described. The patient had a markedly deformed and depressed plaque surrounded by erythema on the right cheek. She also showed linear scleroderma with hair loss on the occipital area and morphea lesions on the neck and shoulder. Histological findings of the facial and other atrophic le...
متن کاملHemimasticatory spasm associated with localized scleroderma and facial hemiatrophy.
OBJECTIVES To report a case and discuss the mechanism of hemimasticatory spasm. DESIGN Case report. PATIENT A 37-year-old woman had a 3-year history of involuntary spasms of the right masseter muscle in association with localized scleroderma and facial hemiatrophy. Electrophysiological studies revealed a normal blink reflex. However, the masseter reflex and silent period were absent on the ...
متن کاملTotal hemiatrophy as a rare presentation of linear scleroderma .
Scleroderma rarely presents as total hemiatrophy of one side of the body. A 63-year-old patient is discussed with progressive facial hemiatrophy and with atrophy of skin, subcutaneous tissue, muscle and bone tissue of one side of the body, complicated by ocular and neurological manifestations.
متن کاملLocalized scleroderma and hemiatrophy in association with antibodies to double-stranded DNA.
Localized scleroderma involves primarily skin but also muscle, bone and synovium. Further associations and transitional forms have been reported. We report here two cases showing associations between localized scleroderma and vasculitis, mononeuritis multiplex, juvenile chronic arthritis and hemiatrophy. In particular our cases both possess antibodies to double-stranded DNA, a finding not previ...
متن کاملLinear scleroderma en coup the sabre, progressive facial hemiatrophy and Rasmussen encephalitis : a single disease spectrum?
Results 9 patients presented with LSCS, followed in 5 of them by progressive hemifacial atrophy (PFH) within 2 years. 3 patients presented with PFH, all 3 had additional scleroderma lesions. Their median(range) age at presentation was 8(4-17)yrs. Extracutaneous manifestations were equally found in LSCS and PFH+LSCS patients. They comprised asymmetry of tooth arches/missing teeth(1), ophthalmolo...
متن کاملذخیره در منابع من
با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید
ژورنال
عنوان ژورنال: The Dublin Journal of Medical Science
سال: 1891
ISSN: 0790-231X
DOI: 10.1007/bf02973007