Rubinstein-Taybi syndrome: principal oral and dental disorders and literature update

نویسندگان

چکیده

Introduction: Oral and dental (OD) disorders in children with Rubinstein-Taybi syndrome (RTS) are frequent but not well-known by dentists pediatricians due to the being extremely rare. Objective: To describe OD findings observed a 5-year-old girl RTS update literature. Clinical case: The patient presented following manifestations: prominent lower lip, narrow mouth opening, arched palate, history of angular cheilitis, micrognathia, poor lingual motility, plaque tartar, bleeding from gingival areas prophylaxis, malocclusion form an anterior open bite. These manifestations seen more than 40-60% patients RTS. Conclusions: Professionals who treat should become aware advisability referring them pediatric dentist 1 year age performing check-ups every 6 months. Dental management is often difficult so collaboration anesthesiologists recommended order carry out safe effective treatment.

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ژورنال

عنوان ژورنال: Iberoamerican journal of medicine

سال: 2021

ISSN: ['2695-5075']

DOI: https://doi.org/10.53986/ibjm.2021.0025