Retroaortic Innominate Vein in Association With Pulmonary Atresia/Major Aortopulmonary Collaterals

BackgroundRetroaortic innominate vein (RAIV) is an extremely rare anomaly of systemic venous return. The prevalence RAIV has been estimated to be 0.02% in individuals without congenital heart disease and 0.5% those with disease. Previous studies have demonstrated association between both conotruncal abnormalities right aortic arch. Our center specializes surgical procedures for patients pulmonary atresia ventricular septal defect major aortopulmonary collateral arteries (PA/VSD/MAPCAs), we frequently observed the presence these patients. purpose this study was evaluate anatomic characteristics RAIV.MethodsThis a single-center retrospective review medical records identify RAIV. period 2002 through 2022, approximately 20,000 evaluated during time frame.ResultsA total 99 were identified Of patients, 64 (65%) had PA/VSD/MAPCAs. Other diagnoses included tetralogy Fallot (n = 16), 3), double outlet ventricle 4), peripheral artery stenosis other 9). In cohort PA/VSD/MAPCAs, 69% arch 30% completely absent central arteries.ConclusionsThe overwhelming majority (90%) abnormalities, PA/VSD/MAPCAs accounting preponderance cases our center.