PULMONARY FUNCTION IN PROGRESSIVE MUSCULAR DYSTROPHY

[Progressive muscular dystrophy].

This paper describes the case of a young man with progressive muscular dystrophy who had supraventricular arrhythmias and intractable congestive failure. Hemodynamic studies and left cineventriculographic findings were compatible with a diagnosis of severe left ventricular failure. Coronary cinearteriography showed an abrupt ending of the artery to the sino-atrial node. At necropsy, a noninflam...

Progressive Muscular Dystrophy (Erb.)

Cardiac and pulmonary complications in Duchenne's progressive muscular dystrophy.

IT IS the purpose of this paper to present a clinical and pathologic study of myocardial involvement in seven previously unreported eases of the Duchenne form of progressive muscular dystrophy. The clinical signs of cardiac involvement in 139 cases and the electrocardiograms taken on the majority of these patients are also discussed. The frequent occurrence of pneumonia has proved to be a serio...

Genetic-epidemiological studies in progressive muscular dystrophy.

A genetic and epidemiological study is especially important in those hereditary diseases for which no effective treatment is known, since then genetic counselling is the only means of prevention. The progressive muscular dystrophies are typical conditions of this sort. Knowledge of the type of hereditary transmission for a given form of muscular dystrophy is the basis for correct genetic progno...

The electrocardiogram in Duchenne progressive muscular dystrophy.

Interpretation of the electrocardiogram in the Duchenne form of progressive muscular dystrophy (PMD) is still debated in the literature. The group studied consisted of 106 patients with the Duchenne type of PMD, aged 3 to 29 years. The duration of the disease varied from a few months to 15 years. One hundred one patients had abnormal electrocardiograms. These were of four types: type a (64 case...