Protein S deficiency: early presentation and pulmonary hypertension.
نویسندگان
چکیده
منابع مشابه
Isolated Protein S Deficiency Presenting as Thromboembolic Pulmonary Arterial Hypertension in a Young Child
A 13 months male child presented with progressive dyspnea of three months and recent cyanosis. Cardio-respiratory examination revealed tachypnea, cyanosis, left parasternal heave and loud P2. Echocardiography revealed thrombus in pulmonary artery and severe pulmonary arterial hypertension. Tests for throbmophilia demonstrated protein S deficiency. Treatment included anticoagulants, sildenafil, ...
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Portal vein thrombosis (PVT) is a common cause of portal hypertension in children. A majority of children with PVT of unknown etiology have functional Protein C deficiency or abnormally elevated levels of anti-cardiolipin antibodies. We report an 8 years old Indian girl with portal cavernoma due to hereditary Protein S deficiency. We documented familial deficiency of Protein S in 2 asymptomatic...
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Two patients with protein C deficiency developed symptomatic pulmonary hypertension secondary to chronic pulmonary embolism. They were successfully treated by thromboendarterectomy.
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Pulmonary hypertension has been observed to be elevated among end-stage renal disease and patients who are on dialysis. Several investigations, have demonstrated that, pulmonary hypertension in end-stage kidney failure patients is related to expressively enhanced mortality and morbidity. Pulmonary hypertension represents a group of comparatively erratic illnesses that causes different pulmonary...
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Background: Vitamin D (Vit D) is linked to various conditions including musculoskeletal, metabolic and cardiopulmonary diseases. However, it is not clear whether correction of vit D deficiency exerts any beneficial effect in patients with pulmonary hypertension. Methods: This study was a prospective uncontrolled longitudinal study. Patients with pulmonary hypertension and vit D d...
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ژورنال
عنوان ژورنال: Archives of Disease in Childhood
سال: 1992
ISSN: 0003-9888,1468-2044
DOI: 10.1136/adc.67.7.960