Poland-Mobius syndrome associated with dextrocardia.

Poland-Möbius syndrome associated with dextrocardia.

A newborn male with Möbius syndrome, Poland anomaly, and dextrocardia is described. This is the second case reported of Poland-Möbius syndrome associated with dextrocardia. The patient presented with strabismus, facial diplegia, difficulty in swallowing, hypoplasia of the left pectoralis major muscle, partial absence of the upper costal cartilages, absence of the left areola, hypoplasia of the ...

The first Korean case of poland-Möbius syndrome associated with dextrocardia

Poland syndrome is characterized by unilateral absence or hypoplasia of the pectoralis muscle and variable degree of ipsilateral hand anomalies. Möbius syndrome is a congenital neurological disorder characterized by complete or partial facial paralysis. Although the pathogeneses of these diseases are not well-characterized, diminished blood flow to the affected side is thought to play a role. A...

Poland anomaly with dextrocardia: a case report.

Poland anomaly was first reported in Guys Hospital report, 1841. Since then many cases have been described. Among the upper limb developmental defects, Poiand anomaly has a prevalence of 1 in 20,000. According to anotherreport 10% of all cases of upper limb syndactyly have Poland anomaly also. Poland anomaly is a sporadic developmental disorder involving the upper limb. Primary defect seems to ...

Rare features associated with Mobius syndrome: Report of two cases

Mobius syndrome is a rare congenital disorder with the preliminary diagnostic criteria of congenital facial and abducent nerve palsy. Involvement of other cranial nerves, too, is common. Prevalence rate of this syndrome is approximately 1 in 100,000 neonates. It is of unknown etiology with sporadic occurrence. However, data regarding the occurrence rate in India is limited. Features such as oro...

Mobius Syndrome and Poland Syndrome Presenting Together in a Single Patient