Pigmentary incontinence (or Bloch-Sulzberger syndrome): a case report in a female infant with epilepsy

Case presentation: Patient L.V.M.B., female, 3 months old, born and resident in Frutal-MG. She was admitted to the Pediatric Emergency Room of Hospital de Clínicas da UFTM, referred from city origin, due an unprecedented convulsive crisis 1 day ago, which characterized by spastic movements topography hemiface on right (right eye traction labial commissure) preceded hyporexia irritability, according mother's report admission. The patient underwent physical examination all segments, but changes were only observed dermatological examination. According report, child had skin since birth, initially it a mild condition composed small hyperchromic papules vesicles located upper limbs. However, there progressive worsening lesions, mainly 7th after with appearance bubbles grouped erythematous base yellowish center, lower limbs, face scalp, predominantly left hemibody (see images 1- 4). At that moment, origin suspicion Impetigo, having been treated antibiotic therapy 4 days, blisters ruptured spontaneously discharged at home. mother reports showed number extent lesions they progressed stage presented Pathological then revealed spongiotic dermatitis eosinophilic exocytosis melanophages superficial dermis, is characteristic Incontinence Pigmenti. Histopathological findings can be seen image 12 (hematoxylin-eosin stain, 40X magnification) 13 14 100X magnification).