Papillon-Lefévre syndrome: a highly-suspected case
نویسندگان
چکیده
منابع مشابه
Papillon-Lefévre syndrome: a highly-suspected case.
Papillon-Lefévre syndrome (PLS) is characterized by severe periodontal disease extending to destruction of the alveolar bone surrounding deciduous teeth and palmoplantar hyperkeratosis of the skin. Increased susceptibility to infection has been reported among individuals with the cathepsin C (CTSC) gene mutation. This article reports a 7-year-old Japanese girl who presented with deciduous tooth...
متن کاملA microbiological study of Papillon-Lefévre syndrome in two patients.
AIM To analyse the microflora of subgingival plaque from patients with Papillon-Lefévre syndrome (PLS), which is a very rare disease characterised by palmar-plantar hyperkeratosis with precocious periodontal destruction. METHODS Bacterial isolates were identified using a combination of commercial identification kits, traditional laboratory tests, and gas liquid chromatography. Some isolates w...
متن کاملPapillon-Lefèvre Syndrome: a case report
Introduction: Papillon-Lefèvre syndrome(PLS) characterized by palmoplantar hyperkeratosis is a rare autosomal recessive genetic disorder with rapidly progressive periodontitis and premature loss of both deciduous and permanent teeth. In this study, we report the clinical and radiographic features of Papillon-Lefèvre syndrome in an 11- year-old girl and we also discuss the history ...
متن کاملPapillon-Lefevre Syndrome: A Case Report
PapillonLefevre syndrome (PLS) is a very rare autosomal recessive disorder characterized by palmoplantar hyperkeratosis and severe early onset of destructive periodontitis leading to premature loss of both primary and permanent dentition.PLS is transmitted as an autosomal recessive condition and consanguinity of parents is evident in about one third of cases. Here we report a case of a 13 year ...
متن کاملPapillon-Lefèvre Syndrome Case Report
1 Assistant professor, Oro-maxillofacial developmental diseases research center, Department of oral medicine, Guilan University of Medical Sciences, Dental school, Rasht, Iran 2 Associate professor, Dental Research Center, Mashhad University of Medical Sciences, Dental School, Mashhad, Iran 3 Assistant professor, Department of Oral and Maxillofacial Radiology, Mashhad University of Medical Scie...
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ژورنال
عنوان ژورنال: Journal of Oral Science
سال: 2006
ISSN: 1343-4934,1880-4926
DOI: 10.2334/josnusd.48.257