Otocephaly: A Case Report of a Rare Congenital Anomaly

Otocephaly is a rare congenital abnormality characterized by the absence or underdevelopment of mandible, misplacement ears towards front, small mouth, and tongue. The syndrome complex otocephaly can be categorized into four types based on associated anomalies. We present case this anomaly in newborn baby delivered 40-year-old woman who presented active labor with premature rupture membranes. Unfortunately, did not survive due to severe respiratory distress, which was consistent clinical features anomaly. rarity poses challenges for both parents healthcare providers. Early antenatal scans are suggested early diagnosis condition. Further research awareness needed better understand manage disorder.