Odontogenic Keratocysts in Nevoid Basal Cell Carcinoma (Gorlin's) Syndrome: CT and MRI Evaluation
نویسندگان
چکیده
منابع مشابه
Odontogenic keratocysts in nevoid basal cell syndrome (Gorlin’s Syndrome). CT and MR evaluation
Introduction: The nevoid basal cell syndrome (Gorlin’s Syndrome) is a dominant autosomic disorder, characterized by multiple basal cell carcinomas, odontegenic keratocysts, dural calcifications, bone and face malformations, tumors including meduloblastoma and ovaric fibromas, as well as different degrees of mental retardation. Characteristic imagine findings of the Gorlin’s Syndrome are odontog...
متن کاملOdontogenic keratocysts in a 5-year-old: initial manifestations of nevoid basal cell carcinoma syndrome.
The purpose of this paper is to report the occurrence of odontogenic keratocysts in a young child. Odontogenic keratocysts are one of the principal features of nevoid basal cell carcinoma syndrome. Their occurrence in this syndrome is usually during the second or third decades of life. This report describes the occurrence of odontogenic keratocysts in a 5-year-old, which proved to be the initia...
متن کاملOdontogenic keratocysts in Nevoid basal cell carcinoma syndrome: a case report
Nevoid basal cell carcinoma syndrome, a rare autosomal dominant disorder, comprises a number of abnormalities such as multiple nevoid basal cell carcinomas, skeletal abnormalities and multiple odontogenic keratocysts. Considering the rarity of this syndrome, we present a 12-year-old boy affected by this syndrome. He had multiple okcs, calcification of falx cerebri, bifid ribs, frontal bossing a...
متن کاملNevoid Basal Cell Carcinoma Syndrome: Report from the Zurich Nevoid Basal Cell Carcinoma Syndrome Cohort.
BACKGROUND Nevoid basal cell carcinoma syndrome (NBCCS, Gorlin-Goltz syndrome) presents various symptoms and can disfigure patients. The estimated prevalence is around 1:100,000. OBJECTIVE To systematically investigate the clinical manifestations of NBCCS patients of the Zurich register and compare them with those described in 4 epidemiological studies performed in other countries. METHODS ...
متن کامل[Gorlin syndrome (nevoid basal cell carcinoma syndrome)].
CLINICAL CASE A 77 year-old male patient with Parkinson's disease and senile dementia had many facial basal cell carcinomas and an ectropion of the left eye. When he experienced respiratory difficulty he was diagnosed to have an ameloblastoma in left nostril requiring surgery. DISCUSSION Gorlin syndrome is an autosomal dominant condition characterized by basal cell carcinomas, and skeletal an...
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ژورنال
عنوان ژورنال: Ear, Nose & Throat Journal
سال: 2004
ISSN: 0145-5613,1942-7522
DOI: 10.1177/014556130408300115