Ocular Inflammatory Disorders in Autoimmune Lymphoproliferative Syndrome (ALPS)

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Rapamycin improves lymphoproliferative disease in murine autoimmune lymphoproliferative syndrome (ALPS).

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autoimmune lymphoproliferative syndrome (alps) in a boy with massive lymphadenopathy

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Autoimmune Lymphoproliferative Syndrome (ALPS) in a Boy with Massive Lymphadenopathy.

Autoimmune lymphoproliferative syndrome (ALPS) is an uncommon nonmalignant lymphoproliferative disease which is characterized by chronic, persistent or recurrent lymphadenopathy, splenomegaly, hepatomegaly, immune cytopenia , hypergammaglobinemia and increased risk of lymphoma. We report a 2-year old boy with hepatosplenomegaly as first presentation. Petechial and purpuric rashes with massive c...

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ژورنال

عنوان ژورنال: Ocular Immunology and Inflammation

سال: 2016

ISSN: 0927-3948,1744-5078

DOI: 10.1080/09273948.2016.1175637