Octreotide in Hennekam syndrome-associated intestinal lymphangiectasia
نویسندگان
چکیده
منابع مشابه
Association of nephrotic syndrome with intestinal lymphangiectasia.
The occurrence of exudative enteropathy in children with the nephrotic syndrome was first reported by Nussle et al. in 1961, but no intestinal pathology has previously been described in nephrotic children, whether with or without protein-losing enteropathy. The finding in small bowel biopsy specimens of intestinal lymphangiectasia, in 4 of 7 cases of nephrotic syndrome, suggests that this assoc...
متن کاملIntestinal Lymphangiectasia
History A three year old boy presented with tetanus who additionally suffered from nonbloody diarrhea. Physical examination showed bilateral edema of the lower limbs. Laboratory data showed iron deficiency anemia, hypoalbuminemia, hypocalcaemia and hypogammaglobulinemia. Stool culture was negative for bacteria however fat droplets were detected in the patient’s stool. Endoscopic examination rev...
متن کاملIntestinal lymphangiectasia.
A 2 year and 11 month old boy presented in December 1994 with a history of recurrent episodes of generalized swelling of the body and loose stools for two years. He had been treated with plasma transfusion and antituberculous treatment in the past. He was the only child to his non-consanguineous parents. At birth, he was noticed to have facial asymmetry. He was breastfed for one year and at adm...
متن کاملIntestinal lymphangiectasia in children
Intestinal lymphangiectasia (IL) is a rare disease characterized by dilatation of intestinal lymphatics. It can be classified as primary or secondary according to the underlying etiology. The clinical presentations of IL are pitting edema, chylous ascites, pleural effusion, acute appendicitis, diarrhea, lymphocytopenia, malabsorption, and intestinal obstruction. The diagnosis is made by intesti...
متن کاملLate-onset primary intestinal lymphangiectasia successfully managed with octreotide: a case report.
We report a case of a patient with late-onset primary lymphangiectasia whose persistent diarrhoea was successfully managed with octreotide. A 63 year-old man visited our clinic with a complaint of worsening general edema. Gastrointestinal endoscopy revealed typical whitish jejunal villi, which suggested primary intestinal lymphangiectasia. Despite a diet, supplemented with medium-chain triglyce...
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ژورنال
عنوان ژورنال: World Journal of Gastroenterology
سال: 2012
ISSN: 1007-9327
DOI: 10.3748/wjg.v18.i43.6333