منابع مشابه
Two Cases of Severe Ochronotic Arthropathy
Ochronotic spondylarthropathy, a long-term musculoskeletal manifestation of alkaptonuria and involvement of joints may lead to a radiographic appearance similar to that of degenerative joint disease. We report the cases of two siblings with progressive familial ochronotic arthropaty treated with total hip arthroplasty.
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Observations and measurements indicate rain often has a major impact on snow slope stability. Measurements to investigate the effects of wetting of low density, alpine snow were made at Snoqualmie Pass, WA, USA. Results indicate that on first wetting, the densification rate can increase by three orders of magnitude. This initial burst of densification occurs independently of the gravitational l...
متن کاملOchronotic arthritis of bilateral knees: a case report.
Alkaptonuria ochronosis is a rare metabolic disease in which the body does not have enough enzyme called homogentisic acid oxidase. Due to the homogentisic acid oxidase deficiency, homogentisic acid accumulates in cartilage and connective tissues which leads to ochronotic arthritis. We reported a case of bilateral ochronotic arthritis verified by clinical presentation, imaging, arthroscopic and...
متن کاملCalcium pyrophosphate dihydrate (CPPD) deposition in ochronotic arthropathy.
The post-mortem examination of an unsuspected case of alkaptonuria revealed extensive ochronosis. Histological examination of undecalcified sections of tracheal, costal, femoral and patellar cartilage revealed, in addition to ochronotic pigment, extensive calcium pyrophosphate dihydrate (CPPD) deposition. Similar deposits were present in intervertebral discs and were related to ossification of ...
متن کاملTotal hip replacement for an ochronotic patient: A technical trick
PATIENT Male, 46 FINAL DIAGNOSIS: Akkaptonuria Symptoms: Hip pain Medication: - Clinical Procedure: Total hip replacement Specialty: Orthopedics and Traumatology. OBJECTIVE Unusual or unexpected effect of treatment. BACKGROUND Ochronosis is an inherited metabolic disease in which there is an accumulation of excessive amounts of homogentisic acid in the connective tissue. As the disease prog...
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ژورنال
عنوان ژورنال: Annals of the Rheumatic Diseases
سال: 1970
ISSN: 0003-4967
DOI: 10.1136/ard.29.5.563-b