Myocardial bridging and sudden death in hypertrophic cardiomyopathy: Salome drops another veil
نویسندگان
چکیده
منابع مشابه
Myocardial bridging and sudden death in hypertrophic cardiomyopathy: Salome drops another veil.
Hypertrophic cardiomyopathy (HCM) is a heterogeneous disease at the clinical, phenotypic, and molecular level. In spite of considerable progress in understanding the disease, many issues continue to be shrouded in mystery, with very slow and often incomplete shedding of the veils, reminiscent of Salome’s dance. These issues include the unpredictable occurrence of sudden cardiac death, the clini...
متن کاملPrevention of Sudden Death in Hypertrophic Cardiomyopathy
C ase presentation: A 14-yearold girl died suddenly and unexpectedly while exercising. Clinical and echocardiographic family screening identified hypertrophic cardiomyopathy (HCM) in her only sibling, an asymptomatic 17-year-old boy. In her brother, echocardiography showed extreme septal ventricular hypertrophy, 35 mm in thickness; left ventricular (LV) outflow obstruction was absent. Left atri...
متن کاملSudden cardiac death risk in hypertrophic cardiomyopathy.
It is well recognized that sudden cardiac death (SCD) is an infrequent, unpredictable, but catastrophic complication of hypertrophic cardiomyopathy (HCM). In population-based studies the overall SCD rate is 1% per year among patients with a clinical diagnosis of HCM. A crucial aspect of the management of patients with HCM is an assessment of each individual patient’s risk for SCD so that preven...
متن کاملSudden cardiac death in hypertrophic cardiomyopathy.
Introduction Hypertrophic cardiomyopathy (HCM) is a common disorder of cardiac muscle associated with sudden cardiac death (SCD). HCM is defined by increased left ventricular wall thickness or mass, in the absence of abnormal loading conditions to account for the observed abnormality. In most adults, the disease is inherited as an autosomal dominant trait and is caused by mutations in cardiac s...
متن کاملApical Hypertrophic Cardiomyopathy in a Case with Chest Pain and Family History of Sudden Cardiac Death: A Case Report
Hypertrophic cardiomyopathy (HCM) is the most common genetic cardiovascular disease, which is caused by a multitude of mutations in genes encoding proteins of the cardiac sarcomere (1). Apical hypertrophic cardiomyopathy (AHCM) is an uncommon type of HCM. The sudden cardiac death is less likely to occur in the patients inflicted with AHCM (2). Herein, we presented the case of a 29-year-old man ...
متن کاملذخیره در منابع من
با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید
ژورنال
عنوان ژورنال: European Heart Journal
سال: 2009
ISSN: 0195-668X,1522-9645
DOI: 10.1093/eurheartj/ehp216