Microvascular imaging of primary erythromelalgia
نویسندگان
چکیده
منابع مشابه
Primary erythromelalgia: case report.
Erythromelalgia is a rare clinical syndrome characterized by heat, redness and intermittent pain in the extremities, being most frequent the bilateral development in the lower extremities. Local cooling brings relief to symptoms, while heating, physical exercises and use of stockings/socks intensify the discomfort. This condition can be primary or idiopathic or secondary to haematological disor...
متن کاملPrimary erythromelalgia: a review
Primary erythromelalgia (PE ORPHA90026) is a rare autosomal dominant neuropathy characterized by the combination of recurrent burning pain, warmth and redness of the extremities. The incidence rate of PE ranges from 0.36 to 1.1 per 100,000 persons. Gender ratio differs according to different studies and no evidence showed a gender preference. Clinical onset of PE is often in the first decade of...
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Erythromelalgia (EM) is a rare disabling clinical syndrome more commonly known to affect the lower extremities. There is no single effective treatment for this disease that often requires a multidisciplinary approach. Herein, we report the case of a 31-year-old woman affected by primary erythromelalgia who was successfully treated with intrathecal Ziconotide. We also observed an unexpected resu...
متن کاملTreatment of primary erythromelalgia with cyclosporine.
A 28-year-old woman presented with severe, persistent burning pain in the legs and feet, with marked erythema, swelling, and warmth (Fig. 1, left-hand panels). The erythema had begun at the age off our years, with no associated disorder. After adolescence, the symptoms became continuous, with erythema that extended to the thighs and the development of live do-like lesions. Burning pain during t...
متن کاملErythromelalgia – A condition caused by microvascular arteriovenous shunting
Chapter 1 Introduction Erythromelalgia (EM) is a rare disorder characterized by red, warm and painful extremities. In what superficially appears to be the antithesis of Raynaud's disease, victims of EM seek relief by cooling of the affected extremity. Over the years terms such as erythermalgia [1], and erythralgia [2] have also been used for the condition. Graves [3] reported the first case of ...
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ژورنال
عنوان ژورنال: Polish Archives of Internal Medicine
سال: 2019
ISSN: 1897-9483
DOI: 10.20452/pamw.14890