Measure of the QT-RR Dynamic Coupling in Patients with the Long QT Syndrome
نویسندگان
چکیده
منابع مشابه
KCNE1 and KCNE2 variants in Patients with Long QT Syndrome
Introduction: Long QT syndrome (LQTS) is a type of ventricular arrhythmia characterized by prolonged QT intervals on electrocardiogram or delay in ventricular repolarization and it can lead to syncope, seizure and sudden cardiac death. Here, KCNE1 and KCNE2 variants are studied among Iranian affected families with this syndrome. Materials and Methods: Fifty patients referring to Rajaei Cardiov...
متن کاملGenotype- and Sex-Specific QT-RR Relationship in the Type-1 Long-QT Syndrome
BACKGROUND Genotype-phenotype investigations have revealed significantly larger risk for cardiac events in patients with type 1 long-QT syndrome (LQT-1), particularly in adult females, with missense mutation in the cytoplasmic loop (C-loop) regions of the α subunit of the KCNQ1 gene associated with an impaired ion channel activation by adrenergic stimulus. We hypothesize that the impaired respo...
متن کاملThe Long QT Syndrome
Introduction The Long QT syndrome (LQTS) can be inherited or acquired and is of particular interest and concern at present. Patients with LQTS are predisposed to the ventricular tachyarrhythmia torsade de pointes (TdP) which causes syncope and sudden death. Inherited LQTS is the prototype of the "primary cardiac arrhythmias" or "cardiac ion channelopathies". The study of inherited LQTS has prov...
متن کاملManagement of Patients with Long QT Syndrome
Long QT syndrome (LQTS) is a rare cardiac channelopathy associated with syncope and sudden death due to torsades de pointes and ventricular fibrillation. Syncope and sudden death are frequently associated with physical and emotional stress. Management of patients with LQTS consists of life-style modification, β-blockers, left cardiac sympathetic denervation (LCSD), and implantable cardioverter-...
متن کاملManagement of patients with long QT syndrome
I have read with great interest the case report entitled “Epicardially placed implantable cardioverter-defibrillator for a child with congenital long QT syndrome” by Sugiyama et al. in the latest issue of the journal [1]. The authors well presented a case of long QT syndrome managed using implantation of an epicardial shock electrode and dose titration of beta-blocker therapy. However, some imp...
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ژورنال
عنوان ژورنال: Annals of Noninvasive Electrocardiology
سال: 2012
ISSN: 1082-720X
DOI: 10.1111/j.1542-474x.2012.00526.x