Lymphoma and cerebral vasculitis in association with X-linked lymphoproliferative disease
نویسندگان
چکیده
منابع مشابه
Lymphoma and cerebral vasculitis in association with X-linked lymphoproliferative disease
Lymphoma is seen in up to 30% of patients with X-linked lymphoproliferative disease (XLP), but cerebral vasculitis related with XLP after cure of Burkitt lymphoma is rarely reported. We describe a case of a 5-year-old boy with XLP who developed cerebral vasculitis two years after cure of Burkitt lymphoma. He had Burkitt lymphoma at the age of 3 years and received chemotherapy (non-Hodgkin's lym...
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Systemic vasculitis is an uncommon manifestation of X-linked lymphoproliferative disease (XLP), a disorder in which there is a selective immune deficiency to Epstein-Barr virus (EBV). The molecular basis for XLP has recently been ascribed to mutations within SLAM-associated protein (SAP), an SH2 domain-containing protein expressed primarily in T cells. The authors describe a patient who died as...
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چکیده ندارد.
X linked lymphoproliferative disease in a United Kingdom family.
X linked lymphoproliferative disease (XLP; Duncan's disease) is a rare disorder affecting boys and characterised by a defective immune response to Epstein-Barr virus caused by a mutation in a gene located at chromosome Xq25. Three siblings with XLP in a single UK family are reported and the variation in phenotypic expression of the disease in these siblings described. One of the siblings with l...
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ژورنال
عنوان ژورنال: Chinese Journal of Cancer
سال: 2013
ISSN: 1000-467X,1944-446X
DOI: 10.5732/cjc.012.10238