LE SYNDROME DE LIMB BODY WALL COMPLEX A PROPOS DUN CAS ET REVUE DE LA LITTERATURE

Limb body wallcomplex (LBWC) is a rare poly malformative syndrome of unknownorigin, comprising major anomalies the ventral wall (thoracoabdominal) associatedwithother anomalies, includingthose limbsthatmay range frompositionaldeformity to agenesis, unusualcraniofacial malformations, and variety visceral thatinclude heart, lungs, genitourinary system. Twophenotypes are describeddepending on feto-placentalattachment. We report case LBWC diagnosed post partum in stillbornwith following malformations: large anterioromphalocele, spina bifida withmeningocele, severescoliosis. The lowerlimbsappearedasymmetricalwithbilateral club feetassociatedwithpolydactyly. stillbirthadheres placenta by very short cord 3 cm 2 arteries vein.