Jerking stiff-man syndrome.
نویسندگان
چکیده
منابع مشابه
Jerking stiff-man syndrome.
A female patient had permanent axial muscular rigidity similar to the "stiff-man syndrome", together with axial myoclonus triggered by stretch reflexes and by supramaximal stimulation of the supraorbital nerve. The disorder responded to treatment with diazepam and baclofen. This disorder bore a marked similarity to the so-called "jerking stiff-man syndrome".
متن کاملA patient with reflex myoclonus and muscle rigidity: "jerking stiff-man syndrome".
A patient with progressive muscular rigidity associated with reflex myoclonus is described. The muscular rigidity was predominantly axial, and the myoclonic jerks affected axial and leg muscles. Jerks occurred either spontaneously, or in response to touch to the perioral region, or to stretch of head and neck muscles. Physiological investigations suggested that the myoclonus originated in the m...
متن کاملStiff man syndrome and related conditions.
The stiff man syndrome (SMS) and its variants, focal SMS, stiff limb (or leg) syndrome (SLS), jerking SMS, and progressive encephalomyelitis with rigidity and myoclonus (PERM), appear to occur more frequently than hitherto thought. A characteristic ensemble of symptoms and signs allows a tentative clinical diagnosis. Supportive ancillary findings include (1) the demonstration of continuous musc...
متن کاملThe 'stiff man syndrome' in a boy.
In October, 1958, a Chinese boy, aged 7 years, was transferred to the Children's Unit with a diagnosis of recurrent tetanus. According to the mother, he had been ill intermittently since 1957 when he was first admitted to hospital complaining of stiffness of the body and inability to open his mouth. He apparently recovered from this illness, but was readmitted on two further occasions with simi...
متن کاملStiff man syndrome with invasive thymic carcinoma.
Stiff man syndrome is a rare disease characterized by painful chronic spasms in the muscle and skeletal system. This syndrome is an autoimmune neurologic disorder which is associated with thymoma. We treated a 32-year-old male patient with a type C thymoma (based on the World Health Organization classification) who had stiff man syndrome. The patient underwent an extended thymectomy which broug...
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ژورنال
عنوان ژورنال: Journal of Neurology, Neurosurgery & Psychiatry
سال: 1982
ISSN: 0022-3050
DOI: 10.1136/jnnp.45.12.1159