Intralabyrinthine sporadic endolymphatic sac tumour
نویسندگان
چکیده
منابع مشابه
Endolymphatic sac tumour in von Hippel-Lindau disease: management strategies
Endolymphatic sac tumour (ELST) is infrequent, as emerges from small series reported in the literature. It is a slow-growing malignancy with local aggressiveness and a low risk of distant metastases. It is often misdiagnosed because of the late onset of symptoms and difficulty in obtaining a biopsy. Its frequency is higher in von Hippel-Lindau (VHL) disease (a genetic systemic syndrome involvin...
متن کاملEndolymphatic sac tumor
Endolymphatic sac tumor is an uncommon, locally aggressive tumor. The tumor is located in the medial and posterior petrosal bone region and may involve the dura. A hypervascular tumor involving the endolymphatic sac with destructive changes, it involves the bone and may show reactive new bone formation. Diagnosis is based on clinical, radiological, and pathological correlation. We present a cas...
متن کاملEndolymphatic sac tumor.
Endolymphatic sac tumor (ELST) is a papillary epithelial neoplasm arising within the endolymphatic sac/duct that shows a high association with von Hippel-Lindau disease (VHL). There is usually a VHL tumor suppressor gene germline mutation with an autosomal dominant inheritance pattern. Approximately 1 in 35,000 to 40,000 people have VHL, of which approximately 10 to 15% have endolymphatic sac t...
متن کاملThe endolymphatic duct and sac.
The endolymphatic duct (ED) and the endolymphatic sac (ES) are the nonsensory components of the endolymph-filled, closed, membranous labyrinth. The ED leads from the utricular and saccular ducts within the vestibule through the vestibular aqueduct (VA) to the ES, which extends through the distal VA out the external aperture of the aqueduct (Fig 1) to terminate in the epidural space of the poste...
متن کاملEffects of endolymphatic sac decompression surgery on endolymphatic hydrops.
CONCLUSIONS The present findings suggest that complete control of vertigo after endolymphatic sac decompression surgery (ESDS) does not always depend on improved vestibular function or reduced endolymphatic hydrops. Vertigo control is, however, associated with hearing stability. OBJECTIVE Among surgical treatments for intractable Meniere's disease, ESDS is performed to preserve and improve in...
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ژورنال
عنوان ژورنال: European Annals of Otorhinolaryngology, Head and Neck Diseases
سال: 2018
ISSN: 1879-7296
DOI: 10.1016/j.anorl.2017.10.002