Interesting case of groenblad-strandberg syndrome
نویسندگان
چکیده
A 40-year old female came with complaints of headache for 5 days. Her general examination and vitals were within normal limits. On complete ophthalmic we found there are irregular streaks radiating from disc in the fundus both eyes suggesting angioid streaks. We did a dermatological evaluation view increased stretchability skin papules over neck & thigh diagnosed as pseudoxanthoma elasticum. So elasticum also known Groenblad-Strandberg syndrome.
منابع مشابه
Intraretinal changes in the Groenblad-Strandberg syndrome.
Systemic elastorrhexis is a widespread hereditary degeneration of mesodermal tissues affecting many structures in the body, particularly the dermis, the media of the arteries, and Bruch's membrane in the eye. Pseudoxanthoma elasticum is one form of elastorrhexis mainly affecting the skin. Degeneration of the elastic lamina of Bruch's membrane results in the formation of angioid streaks in the r...
متن کاملIntraretinal changes in the Groenblad - Strandberg syndrome WASIF KADRI , EMANUEL
Systemic elastorrhexis is a widespread hereditary degeneration of mesodermal tissues affecting many structures in the body, particularly the dermis, the media of the arteries, and Bruch's membrane in the eye. Pseudoxanthoma elasticum is one form of elastorrhexis mainly affecting the skin. Degeneration of the elastic lamina of Bruch's membrane results in the formation of angioid streaks in the r...
متن کاملIntraretinal changes in the Groenblad - Strandberg syndrome WASIF KADRI
Systemic elastorrhexis is a widespread hereditary degeneration of mesodermal tissues affecting many structures in the body, particularly the dermis, the media of the arteries, and Bruch's membrane in the eye. Pseudoxanthoma elasticum is one form of elastorrhexis mainly affecting the skin. Degeneration of the elastic lamina of Bruch's membrane results in the formation of angioid streaks in the r...
متن کاملA Grönblad-Strandberg syndrome.
Tyndall effect, it will allow fluorescein to pass through. Thus the fluorescein will give an earlier and more sensitive impression. 1! L The most recent trends here are aimed at finding out the effect of pathological aqueous on a tissue culture of fibrocytes. It is suspected from clinical observations that the pathological humour will have a detrimental effect on theSe cells. The work has only ...
متن کاملPseudoxanthoma elasticum (Grönblad-Strandberg syndrome).
Pseudoxanthoma elasticum (PXE) is a rare disorder of elastin which primarily involves the skin, cardiovascular system, and eyes, but also manifests in the central nervous system, skeleton, and gastrointestinal tract. Rigall first described the cutaneous lesions of PXE in 1881 and thought the disorder was akin to the xanthomatoses. In 1896, Darier2 showed the typical histological changes in elas...
متن کاملذخیره در منابع من
با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید
ژورنال
عنوان ژورنال: Indian Journal of Clinical and Experimental Ophthalmology
سال: 2022
ISSN: ['2395-1443', '2395-1451']
DOI: https://doi.org/10.18231/j.ijceo.2022.115