Increased Washout of <sup>123</sup>I-BMIPP in Triglyceride Deposit Cardiomyovasculopathy (TGCV) with Severe Coronary Stenosis
نویسندگان
چکیده
منابع مشابه
Quantitative proteomic analysis of cultured skin fibroblast cells derived from patients with triglyceride deposit cardiomyovasculopathy
BACKGROUND Triglyceride deposit cardiomyovasculopathy (TGCV) is a rare disease, characterized by the massive accumulation of triglyceride (TG) in multiple tissues, especially skeletal muscle, heart muscle and the coronary artery. TGCV is caused by mutation of adipose triglyceride lipase, which is an essential molecule for the hydrolysis of TG. TGCV is at high risk for skeletal myopathy and hear...
متن کاملPeripheral leukocyte anomaly detected with routine automated hematology analyzer sensitive to adipose triglyceride lipase deficiency manifesting neutral lipid storage disease with myopathy/triglyceride deposit cardiomyovasculopathy
Adipose triglyceride lipase (ATGL) deficiency manifesting neutral lipid storage disease with myopathy/triglyceride deposit cardiomyovasculopathy presents distinct fat-containing vacuoles known as Jordans' anomaly in peripheral leucocytes. To develop an automatic notification system for Jordans' anomaly in ATGL-deficient patients, we analyzed circulatory leukocyte scattergrams on automated hemat...
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BACKGROUND Body iron status has been implicated in atherosclerotic cardiovascular disease. The main hypothesis is that high iron status is associated with increased oxidation of LDL. We investigated the potential role of ferritin as an additional risk factor promoting atherosclerosis among a young population with coronary artery disease (CAD). METHODS Four hundred consecutive patients (218 ma...
متن کاملResting 123I-BMIPP scintigraphy for detection of organic coronary stenosis and therapeutic outcome in patients with chest pain.
PURPOSE Resting 123I-BMIPP scintigraphy can detect coronary artery disease based on persistent abnormality of myocardial fatty acid metabolism after transient ischemia. The present study aimed to determine the value of resting 123I-BMIPP scintigraphy in diagnosing coronary artery disease and predicting the therapeutic outcome in patients with chest pain symptom. METHOD Five hospitals particip...
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A 33-year-old female presented with the typical angina symptoms of dyspnea on exertion. Five years prior, the patient had been diagnosed with familial hypercholesterolemia, as had her living siblings (a brother and a sister). The patient’s family history included 2 brothers and 2 sisters that died in childhood due to unknown etiology. Although she was being treated with 80 mg atorvastatin and 1...
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ژورنال
عنوان ژورنال: Annals of Nuclear Cardiology
سال: 2019
ISSN: 2189-3926,2424-1741
DOI: 10.17996/anc.19-00106