Hypertrophic cardiomyopathy, noncompaction cardiomyopathy, or noncompaction phenotype: another diagnosis, another further treatment

Noncompaction cardiomyopathy: A rare cardiomyopathy

Introduction: Noncompaction cardiomyopathy (NccM) is a rare form of cardiomyopathy. the American Heart Association classified it as a genetic cardiomyopathy. the pathogenesis of this condition is attributed to the failure of trabecular myocardium to compact and underdeveloped microcoronary circulation. case report: We present a case of a 72-year-old African American female who presented with sh...

Noncompaction cardiomyopathy: a current view.

Isolated non-compaction cardiomyopathy is a rare disease that is likely to develop in the embryonic period. It is caused by the intrauterine arrest of the myocardial compaction process in the beginning of the fetal development. It is characterized by prominent myocardial trabeculations and deep intertrabecular recesses, as well as the thickening of the myocardium into two distinct layers (compa...

Adult bi-ventricular noncompaction cardiomyopathy.

Limitations in the Diagnosis of Noncompaction Cardiomyopathy by Echocardiography

Limitations in the Diagnosis of Noncompaction Cardiomyopathy by Echocardiography Viviane Tiemi Hotta,1,2 Sabrina Cunha Tendolo,2 Ana Clara Tude Rodrigues,3,4 Fábio Fernandes,2 Luciano Nastari,2 Charles Mady2 Instituto do Coração (InCor) do Hospital das Clínicas da Faculdade de Medicina da Universidade de São Paulo (HCFMUSP);1 Fleury Medicina e Saúde;2 Hospital das Clínicas – FMUSP;3 Hospital Is...

Noninvasive and invasive evaluation of noncompaction cardiomyopathy.

Noncompaction cardiomyopathy is a recently described rare congenital cardiomyopathy; patients can be asymptomatic or develop diastolic and/or systolic left ventricular dysfunction with heart failure, systemic emboli or ventricular arrhythmias. Long-term prognosis is poor. Currently, diagnosis is based on findings on 2D echocardiography; in the current case report we demonstrate the use of MRI t...