Hepatopulmonary Syndrome Due to Congenital Extrahepatic Portosystemic Shunts: A Case Report
نویسندگان
چکیده
Congenital extra hepatic port systemic shunt, is a rare clinical entity which can lead to hepatopulmonary syndrome wherein blood from portal vein directly drains into circulation, causing an alteration in metabolism of pulmonary vasoactive substances, vasodilatation, diffusion-perfusion defects, and eventually, arterial hypoxemia due either increase vascular resistance or the creation arteriovenous malformations.
منابع مشابه
A Rare Cause of Cyanosis: Hepatopulmonary Syndrome Caused by Congenital Extrahepatic Portosystemic Shunt
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Congenital extrahepatic portosystemic shunt (CEPS) is a rare disorder characterised by partial or complete diversion of portomesenteric blood into systemic veins via congenital shunts. Type I is characterised by complete lack of intrahepatic portal venous blood flow due to an end to side fistula between main portal vein and the inferior vena cava. Type II on the other hand is characterised by p...
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ژورنال
عنوان ژورنال: Archives of pediatric surgery
سال: 2022
ISSN: ['2643-5721']
DOI: https://doi.org/10.36959/472/367