Giant elephantiasis neuromatosa in the setting of neurofibromatosis type 1: A case report
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چکیده
منابع مشابه
Giant elephantiasis neuromatosa in the setting of neurofibromatosis type 1: A case report.
Elephantiasis neuromatosa (EN) can arise from a plexiform neurofibroma of the superficial and deep nerves developing from a hyperproliferation of the perineural connective tissue infiltrating adjacent fat and muscles. To date, the clinical association between EN and neurofibromatosis type 1 (NF1) has been poorly defined, particularly with regard to the role of lymphatic alterations and the cons...
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ژورنال
عنوان ژورنال: Oncology Letters
سال: 2016
ISSN: 1792-1074,1792-1082
DOI: 10.3892/ol.2016.4469