Facial Plexiform Neurofibromatosis Type I
نویسندگان
چکیده
منابع مشابه
Prevalence of plexiform neurofibroma in children and adolescents with type I neurofibromatosis.
OBJECTIVE To assess prevalence of plexiform neurofibroma in children and adolescents with type I neurofibromatosis and its malignant potential. METHODS A retrospective study was conducted through analysis of the database at Centro Nacional de Neurofibromatose [Brazilian Neurofibromatosis Center], collected from the following reference services between 1996 and 2004: Instituto de Dermatologia ...
متن کاملResection of small plexiform neurofibromas in neurofibromatosis type 1 children
BACKGROUND: Plexiform neurofibromas (PNF) are benign tumors of the peripheral nerve which mostly develop in patients with neurofibromatosis type 1 (NF1). Surgical interventions are usually not applied to children with small tumors. These are rather restricted to debulking of larger tumors in adults that cause clinical complications or aesthetic disfigurement. In most cases, a total resection of...
متن کاملCutaneous plexiform schwannomas in a patient with neurofibromatosis type 2.
Plexiform schwannoma is a rare benign neoplasm of the neural sheath characterized by a multinodular plexiform growth pattern. The tumor usually occurs as an isolated finding, although rare cases have been reported in association with neurofibromatosis type 2 (NF2). A 25-year-old man was admitted for foot drop. He had an asymptomatic skin-colored nodule on his neck that had been present for 10 y...
متن کاملPlexiform neurofibroma in the ear canal of a patient with type I neurofibromatosis.
A neurofibromatose tipo 1 (NF-1) é uma doença genética multissistêmica que apresenta importantes manifestações cutâneas, tais como manchas café-com-leite, efélides e neurofibromas. A incidência de NF-1 é de aproximadamente 1:2500 novos nascimentos, incidindo em todas as raças e afetando igualmente ambos os sexos. A estimativa é de que existam hoje, no Brasil, cerca de 80.000 casos e, no mundo, ...
متن کاملOral plexiform neurofibroma not associated with neurofibromatosis type I: case report.
An unusual case of isolated plexiform neurofibroma arising in the oral cavity without other clinical manifestations or family history of neuro-fibromatosis-1 (NF-1) is described. The tumor was histopathologically analyzed and an immunohistochemical panel comprising S-100 protein, epithelial membrane antigen (EMA), collagen IV, and CD34 was performed. Typical features of plexiform neurofibroma c...
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ژورنال
عنوان ژورنال: Bengal Journal of Otolaryngology and Head Neck Surgery
سال: 2018
ISSN: 2395-2407,2395-2393
DOI: 10.47210/bjohns.2018.v26i2.170