DYSPLASTIC GANGLIOCYTOMA OF THE CEREBELLUM (LHERMITTE-DUCLOS SYNDROME) : A CASE REPORT
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چکیده
منابع مشابه
Lhermitte-Duclos Disease (Dysplastic Cerebellar Gangliocytoma) in a Young Patient
Lhermitte Duclos disease also called dysplastic gangliocytoma of cerebellum is an extremely rare cerebellar neoplasm. It usually presents with raised intracranial pressure along with cerebellar signs. We report a rare case of Lhermitte Duclos disease of a 20 years male who presented with signs & symptoms of raised intracranial tension. CT features were suggestive of Lhermitte-Duclos disease. Su...
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Lhermitte-Duclos disease (LDD; dysplastic cerebellar gangliocytoma) is a rare hamartomatous lesion of the cerebellar cortex and this was first described in 1920. LDD is considered to be part of the autosomal-dominant phacomatosis and cancer syndrome Cowden disease (CS). We examined the brain of a 46-year-old man, who displayed the manifestations of CS, with 7 Tesla (T) and 1.5 T MRI and 1.5 T M...
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Lhermitte-Duclos disease (LDD) or dysplastic gangliocytoma of the cerebellum is a rare benign lesion of uncertain pathogenesis characterized by overgrowth of cerebellar ganglion cells which replace granular cells and Purkinje cells; this results in gross thickening of the cerebellar folia. It is revealed by symptoms of raised intracranial pressure, cerebellar impairment and obstructive hydrocep...
متن کاملLhermitte-duclos Disease in a Young Adult Case Report
Dysplastic gangliocytoma of the cerebellum is a very rare lesion. The other names assigned to this pathology are Lhermitte-Duclos disease. ganglioneuroma. hamartoma of the cerebellum. purkengioma. granule cell hypertrophy or granulomolecular hypertrophy of the cerebellum. Only few cases have been reported in the literature (1-20).since the first report by Lhermitte and Duclos (11).Clinically. t...
متن کاملLhermitte – Duclos Disease in a Young Adult: Rare Entity
Lhermitte - Duclos disease also called dysplastic gangliocytoma of cerebellum is an extremely rare cerebellar lesion which share features of both malformation and neoplasm. The usual presentation is of raised intracranial pressure along with cerebellar signs. We report a case of 23 year male who presented with headache & diplopia. MRI was suggestive of the diagnosis. Subtotal excision of th...
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ژورنال
عنوان ژورنال: International Journal of Advanced Research
سال: 2020
ISSN: 2320-5407
DOI: 10.21474/ijar01/11240