Desmoplastic small round cell tumour: the radiological, pathological and clinical features
نویسندگان
چکیده
منابع مشابه
Desmoplastic small round cell tumour: the radiological, pathological and clinical features
OBJECTIVES Desmoplastic small round cell tumours (DSRCTs) are rare aggressive tumours of young adults that present late and have poor prognosis. This review discusses distinctive radiological features, histopathology and clinical course of this soft-tissue sarcoma. METHODS From 1991 to 2012, the radiology of 20 patients with pathologically proven DSRCT was independently reviewed by two experi...
متن کاملDesmoplastic small round cell tumour: Cytological and immunocytochemical features
BACKGROUND: Desmoplastic small round cell tumor (DSRCT) is a rare and highly aggressive neoplasm. The cytological diagnosis of these tumors can be difficult because they show morphological features quite similar to other small round blue cells tumors. We described four cases of DSRCT with cytological sampling: one obtained by fine needle aspiration biopsy (FNAB) and three from serous effusions....
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Submit Manuscript | http://medcraveonline.com complaints of something moving in the abdomen for the past two months. On physical examination, there was a palpable lump in the right periumbilical area about 5 x 4 cm in size, which was non tender, mobile, firm in consistency and smooth margins. Rest of abdominal examination was normal. The routine haematological and biochemistry investigations we...
متن کاملDesmoplastic Small Round Cell Tumour of Childhood: A Report of Four Cases Demonstrating Wider Clinical Features and Variable Outcome
Purpose. Four further cases of desmoplastic small round cell tumour with multi phenotypic differentiation are described.Subjects. Two patients were typical (male, adolescent with peritoneal tumour and, in one case, liver metastases) and did not respond well to treatment. Two other patients showed less usual features (young, female with retroperitoneal disease, both with intraspinal extension an...
متن کاملIntra-abdominal desmoplastic small round cell tumor
BACKGROUND The desmoplastic small round cell tumour is a rare and aggressive intra-abdominal neoplasia, with only 200 cases reported, and a higher incidence in men and predilection for the second decade of life. Histologically characterized by the presence of small nests of undifferentiated tumour cells, wrapped in fibrous desmoplastic stroma. CLINICAL CASE A 24 year old male started with abd...
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ژورنال
عنوان ژورنال: Insights into Imaging
سال: 2013
ISSN: 1869-4101
DOI: 10.1007/s13244-012-0212-x