Coexistent Primary Biliary Cholangitis with CREST Syndrome (Reynolds Syndrome)
نویسندگان
چکیده
منابع مشابه
Primary biliary cirrhosis and CREST syndrome.
of the skin folds of her face and a lack of ability to open her mouth. Her limbs showed sclerodactyly and isolated telangiectases (Fig. 1a). She had positive anticentromere antibody. She was evaluated because of dysphagia with solids, pyrosis and regurgitation. The esophageal manometry showed a hypotensive lower esophageal sphincter and peristaltic waves of low amplitude in the body of the esop...
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of the carbohydrate side chains. Thus, we feel that data obtained using different methods should be compared very cautiously. In our hands, the use of formalin fixed tissues has given the most reproducible results. As far as the persistence of changes in lectin binding pattern after gluten free diet, Barresi et al provide very interesting and exciting results. We agree that further studies on t...
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BACKGROUND Overlap syndrome has been introduced to the field of hepatology to describe the coexistence of two or more autoimmune hepatic conditions in the same individual. This is a rare clinical case of a patient diagnosed with primary biliary cirrhosis (PBC) who later developed primary sclerosing cholangitis (PSC). This is a unique case as no other cases with a similar pattern have been repor...
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ژورنال
عنوان ژورنال: The American Journal of Medicine
سال: 2017
ISSN: 0002-9343
DOI: 10.1016/j.amjmed.2017.05.019