Clinical, radiographic and lung function features of diffuse congenital cystic adenomatoid malformation of the lung in an adult
نویسندگان
چکیده
منابع مشابه
Clinical, radiographic and lung function features of diffuse congenital cystic adenomatoid malformation of the lung in an adult.
Congenital cystic adenomatoid malformation of the bronchi with bilateral lung involvement has only previously been reported in one possible adult case. This report describes a young man with bilateral diffuse lung involvement, characteristic histological features, and a mixed restrictive/obstructive lung function pattern.
متن کاملCongenital Cystic Adenomatoid Malformation of the Lung
Congenital cystic adenomatous malformations (CCAMs) of the lung represent the most common lung defect diagnosed prenatally. CCAMs are intrapulmonary lesions with a typical hyperechoic appearance on ultrasound (US), with or without cystic components. Both sides of the lung, both sexes, and all races are equally affected. Most fetuses with CCAM are detected prenatally and have a good outcome, but...
متن کاملCongenital cystic adenomatoid malformation of the lung.
Ultrastructural study of a congenital cystic adenomatoid malformation of the lung revealed a persistence of type 2 pneumocytes lining the alveolar and gland-like spaces. The larger cystic areas were lined by normal bronchiolar-type epithelium and were surrounded by a few smooth muscle cells. The interstitium contained undifferentiated mesenchymal cells. No cartilage or bronchial glands were pre...
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Congenital cystic Adenomatoid malformation is a rare developmental abnormality of the lung occuring in 1-4/100000 live births.In most cases the outcome with CCAM in fetus is very good,while in some cases the outcome is very bad and can be life threatning for the fetus.we report here a case of 40 day old female infant who presented with worsening respiratory distress since birth and x ray and CT...
متن کاملCongenital cystic adenomatoid malformation of the left lung presenting in an adult.
Haemogram and biochemical tests were normal. Chest radiograph (postero-anterior view) showed shift of the mediastinum to the left with multiple cavities on the same side and contra-lateral compensatory hyperinflation (Figure 1). Sputum smears were negative for acid-fast bacilli on two occasions. High resolution computed tomography (HRCT) (Figure 2) showed mediastinal shift to the left and eleva...
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ژورنال
عنوان ژورنال: European Respiratory Journal
سال: 1997
ISSN: 0000-0000,0903-1936
DOI: 10.1183/09031936.97.10071680