Carney complex and other conditions associated with micronodular adrenal hyperplasias
نویسندگان
چکیده
منابع مشابه
Multiple osteoblastomas in a child with Cushing syndrome due to bilateral adrenal micronodular hyperplasias
Adrenocorticotropin-independent adrenal hyperplasias are rare diseases, which are classified into macronodular (>1 cm) and micronodular (≤1 cm) hyperplasia. Micronodular adrenal hyperplasia is subdivided into primary pigmented adrenocortical disease and a limited or nonpigmented form 'micronodular adrenocortical disease (MAD)', although considerable morphological and genetic overlap is observed...
متن کاملAdrenal pathophysiology: lessons from the Carney complex.
The Carney complex (CNC) is a dominantly inherited syndrome responsible mainly for spotty skin pigmentation (lentiginosis), endocrine overactivity, and cardiac myxomas. Adrenocorticotropic hormone independent Cushing's syndrome due to primary pigmented nodular adrenocortical disease (PPNAD) is a main characteristic of CNC. PPNAD is a very rare cause of Cushing's syndrome due to a primary bilate...
متن کاملAdrenal Cortex Tumors and Hyperplasias
The adrenal cortex tumors include both malignant adrenal cortex cancers (ACC) and benign masses (ACT) that can be either secreting, of one of the hormones normally produced in the adrenal cortex (Cushing’s syndrome if the hypersecretion is of cortisol or Conn’s syndrome if it is aldosterone) or non-secretory (Incidentalomas). The outer part of the adrenal glands, the adrenal cortex, is responsi...
متن کامل[Carney complex].
Carney complex (CNC) is an autosomal dominantly inherited syndrome characterized by spotty skin pigmentation, cardiac and cutaneous myxoma, and endocrine overactivity. Skin pigmentation includes lentigines and blue nevi. Myxomas may occur in breast, skin and heart. Cardiac myxomas may be multiple and occur in any cardiac chamber, and are more prone to recurrence. The most common endocrine gland...
متن کاملمعرفی یک مورد سندرم Carney Complex
سندرم کارنی (Carney Complex) یک سندرم اتوزومال غالب است که با تومورهای مختلف شامل میکزوما در محل‌های متفاوت، تومورهای اندوکرین و ضایعه‌های لنتیگو مشخص می‌شود و تاکنون در ایران گزارش نشده است. بیماری که دراین مقاله معرفی می‌شود، زن 27 ساله‌ای است که با علایم درد پهلو، مراجعه کرده بود. در معاینه با توجه به علایم هیرسوتیسم، چاقی تنه‌ای، هیپرپیگمانتاسیون و هیپرتانسیون، سندرم کوشینگ مطرح شد و با آزم...
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ژورنال
عنوان ژورنال: Best Practice & Research Clinical Endocrinology & Metabolism
سال: 2010
ISSN: 1521-690X
DOI: 10.1016/j.beem.2010.10.006