Autopsy findings in a case of idiopathic pleuroparenchymal fibroelastosis: A rare entity with review of literature

Idiopathic pleuroparenchymal fibroelastosis is a rare idiopathic interstitial pneumonia which mainly affects the upper lobe of lungs resulting in intra alveolar fibrosis, elastosis and visceral pleural fibrosis. For definite diagnosis, radiographic findings as well histopathology are required. The overlap with lung diseases seen usually, makes it challenging to diagnose. There no guidelines available for diagnosis appropriate management this disease only few cases reported literature. We report case autopsy 32-year-old female who allegedly died heart failure review