Arterial complications of vascular Ehlers-Danlos syndrome
نویسندگان
چکیده
منابع مشابه
Vascular Complications of Ehlers-Danlos Syndrome in Young Chinese Adults
Arterial dissection is uncommon in young adults and there are usually underlying causes. This report describes 2 young patients with vascular complications after trivial injury who were diagnosed to have Ehlers-Danlos syndrome. One patient died while the other remains in a stable condition. Early clinical recognition of this syndrome is necessary so as to prevent mortality and reduce morbidity.
متن کاملGastrointestinal complications of the Ehlers-Danlos syndrome.
The gastrointestinal abnormalities encountered in 125 patients with the Ehlers-Danlos syndrome have been described. Spontaneous perforation of the intestine and massive gastrointestinal haemorrhage are uncommon but potentially lethal complications of the Ehlers-Danlos syndrome. Less dangerous abnormalities, such ;as external hernia, hiatus hernia, eventration of the diaphragm, intestinal divert...
متن کاملLethal complications of the Ehlers-Danlos syndrome.
Death from arterial bleeding or gastrointestinal perforation has previously been reported in more than 15 patients with the Ehlers-Danlos syndrome. On a basis of 100 personally examined patients and a review of published accounts, these events seem particularly likely to occur in two distinct and recognizable forms (the gravis and the ecchymotic forms) of the syndrome.
متن کامل[Ehlers-Danlos syndrome].
We have described a patient with type 4 Ehlers-Danlos syndrome who died of a ruptured pulmonary artery. Of the six subtypes of Ehlers-Danlos syndrome, which can usually be clinically differentiated, only types 1 and 4 appear to be associated with a substantial risk of arterial rupture.
متن کاملEhlers-Danlos syndrome: complications and solutions concerning anesthetic management.
Ehlers-Danlos syndrome is an inherited disorder that results in dysfunctional collagen bundles. These dysfunctional collagen bundles are most noticeable in tissues rich with collagen fibers--skin, vessels, GI, and ligaments. Until gene therapy advancements can correct the underlying gene mutations causing faulty collagen, the mainstay of treatment is prevention of traumatic injury. The success ...
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ژورنال
عنوان ژورنال: Journal of Vascular Surgery
سال: 2016
ISSN: 0741-5214
DOI: 10.1016/j.jvs.2016.06.120