Arrhythmogenic Cardiomyopathy: A Disease or Merely a Phenotype?
نویسندگان
چکیده
منابع مشابه
Arrhythmogenic cardiomyopathy
Arrhythmogenic cardiomyopathy is an inherited heart muscle disorder, predisposing to sudden cardiac death, particularly in young patients and athletes. Pathological features include loss of myocytes and fibrofatty replacement of right ventricular myocardium; biventricular involvement is often observed. It is a cell-to-cell junction cardiomyopathy, typically caused by genetically determined abno...
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An 8-month-old Labrador retriever bitch was evaluated for sudden-onset, progressive abdominal distension. Physical examination revealed an exaggerated inspiratory effort, severe ascites, bilateral jugular vein distension, and hypokinetic femoral arterial pulses. Thoracic auscultation detected tachycardia with muffled heart sounds, without audible cardiac murmurs. Thoracic radiographs identified...
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Arrhythmogenic right ventricular dysplasia (ARVD) is a recently described entity characterized by right ventricular myopathic changes and right ventricular tachycardia. The presence or extent of left ventricular dysfunction in ARVD is not known. We assessed right ventricular and left ventricular function and size in six patients with ARVD by echocardiography and radionuclide angiocardiography d...
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Right ventricular dysplasia is being recognized with increasing frequency. It should be considered as a cause of ventricular tachycardia of left bundle branch block configuration and/or sudden unexpected death particularly during exercise in young men. The electrocardiogram (ECG) may show anterior precordial T wave inversion, particularly in lead V2 and/or a QRS complex duration > or = 110 ms i...
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Advances in cardiovascular imaging increasingly afford unique insights into heritable myocardial disease. Because the clinical presentation of genetic cardiomyopathies may range from nonspecific symptoms to sudden cardiac death, an accurate diagnosis has implications for individual patients as well as related family members. The initial consideration of genetic cardiomyopathy may occur in the i...
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ژورنال
عنوان ژورنال: European Cardiology Review
سال: 2020
ISSN: 1758-3764,1758-3756
DOI: 10.15420/ecr.2019.05