Anesthetic Management of a Pediatric Patient with Leigh Syndrome
نویسندگان
چکیده
منابع مشابه
Anesthetic management of a pediatric patient with Leigh syndrome.
BACKGROUND AND OBJECTIVES Leigh syndrome (LS) is a rare disease caused by abnormalities of mitochondrial energy generation. The central nervous system is most frequently affected, with psychomotor underdevelopment, seizures, nystagmus, ophthalmoparesis, optic atrophy, ataxia, dystonia, or respiratory failure. Surgical and anesthetic procedures stimulate the tracheal irritability, and could exac...
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Leigh syndrome (LS) is a rare disease mainly affecting the central nervous system due to the abnormalities of mitochondrial energy generation and seen in early childhood with progressive loss of movement, mental abilities, seizures, nystagmus, ophthalmoparesis, optic atrophy, ataxia, dystonia, or respiratory failure. Anesthesia and surgery exacerbate the risks of aspiration, wheezing, and breat...
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Corresponding author: Joon-Ho Lee, M.D., Ph.D., Department of Anesthesiology and Pain Medicine, Bucheon Hospital, Soonchunhyang University, 1174, Jung-dong, Wonmi-gu, Bucheon 420-767, Korea. Tel: 82-32-621-5340, Fax: 82-32-621-5322, E-mail: [email protected] This is an open-access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http:// creativec...
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ژورنال
عنوان ژورنال: Brazilian Journal of Anesthesiology
سال: 2013
ISSN: 0034-7094
DOI: 10.1016/s0034-7094(13)70219-8