Anderson–Fabry disease
نویسندگان
چکیده
منابع مشابه
Myocardial strain in a health and disease: CMR feature tracking analysis in cardiac hypertrophy
Methods Ninety-five healthy volunteers, 45 patients with AndersonFabry disease (AFD), 48 with hypertension (HT), 65 with hypertrophic cardiomyopathy (HCM), 62 with severe aortic stenosis (AS), 85 with systemic amyloidosis (AMY) were enrolled. Longitudinal and transversal strain was calculated from 3 long-axis cine views, circumferential and radial strain from 3 short-axis cine images using a de...
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The advent of enzyme replacement therapy for AndersonFabry disease (AFD) adds impetus for the early detection of patients with this inherited multiorgan lipid storage disease. The resultant accumulation of neutral glycosphingolipids, especially globotriaosylceramide (Gb3), in various cell types promotes development of disease-related complications associated with renal, cardiovascular, and cere...
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ژورنال
عنوان ژورنال: Journal of Cardiovascular Medicine
سال: 2018
ISSN: 1558-2027
DOI: 10.2459/jcm.0000000000000637