An adult with episodic retrosternal chest pain: an unusual presentation of congenital pulmonary airway malformation – case report

Abstract Background Congenital pulmonary airway malformation (CPAM) with partial anomalous venous connection presenting as episodic retrosternal chest pain on exertion in an adult has not been described. Case presentation A 21-year-old female, non-smoker, presented a 4-year history of sharp, episodic, pains brought exercise. contrast-enhanced computed tomography (CT) scan showed grossly overinflated left lower lobe drainage into the hemi-azygos vein. Lobectomy, recommended treatment choice, carried out thoracoscopically, was curative satisfactory mid-term results. Histology confirmed type-II congenital malformation. Conclusions CPAM can present young adults unusual symptoms exertion. When suspected CT is gold standard for establishing diagnosis. An anatomical lung resection medium term