منابع مشابه
Infantile myofibromatosis*
Infantile myofibromatosis is a mesenchymal disorder characterized by the fibrous proliferation of the skin, bone, muscle and viscera. It is the most common fibrous tumor in childhood. We present a newborn with skin and bone disease without visceral involvement, who showed good response to vinblastine and methotrexate. Clinical features, etiology, diagnosis, and treatment are reviewed.
متن کاملInfantile Myofibromatosis
Infantile myofibromatosis (IMP) is a rare tumour with a wide spectrum of disease activity ra a solitarY cutaneous nodule through to a multicentric form ,vith widespread visceral involveluent. R is charactelised by its unique ability to spontaneously regress and has a typical histological appearance of a~tin-positivefibroblasts arranged in whorls or fascicles and vessels in a pericytomatous patt...
متن کاملInfantile myofibromatosis.
Infantile myofibromatosis (IMF) is a rare tumour with a wide spectrum of disease activity ranging from a solitary cutaneous nodule through to a multicentric form with widespread visceral involvement. It is characterised by its unique ability to spontaneously regress and has a typical histological appearance of actin-positive fibroblasts arranged in whorls or fascicles and vessels in a pericytom...
متن کاملMulticentric Infantile Myofibromatosis
We present a case of multicentric infantile myofibromatosis in a 3-month-old male infant who had multiple papular lesions on his extremities and trunk and a slowly growing and bulging mass on his left occipital area since birth. His general physical condition was good and psychomotor development was normal. The diagnosis was established by histopathological and immunohistochemical studies along...
متن کاملCT of infantile myofibromatosis of the orbit with intracranial involvement: a case report.
An infant boy presented at birth with a large mass protruding from the left orbit that significantly displaced the left globe laterally and inferiorly . Biopsy of the mass was performed the next day, yielding the diagnosis of infantile myofibromatosis. Therapy was considered but the parents opted for no treatment, although they agreed to yearly CT follow-up examinations. The CT study at the tim...
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ژورنال
عنوان ژورنال: Molecular and Cellular Pediatrics
سال: 2021
ISSN: 2194-7791
DOI: 10.1186/s40348-021-00117-9