Adjusting diet with sapropterin in phenylketonuria: what factors should be considered?
نویسندگان
چکیده
منابع مشابه
Adjusting diet with sapropterin in phenylketonuria: what factors should be considered?
The usual treatment for phenylketonuria (PKU) is a phenylalanine-restricted diet. Following this diet is challenging, and long-term adherence (and hence metabolic control) is commonly poor. Patients with PKU (usually, but not exclusively, with a relatively mild form of the disorder) who are responsive to treatment with pharmacological doses of tetrahydrobiopterin (BH4) have either lower concent...
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ژورنال
عنوان ژورنال: British Journal of Nutrition
سال: 2011
ISSN: 0007-1145,1475-2662
DOI: 10.1017/s0007114511000298