Acquired amegakaryocytic thrombocytopenia purpura and eosinophilic fasciitis: A long relapsing and remitting course
نویسندگان
چکیده
منابع مشابه
[Relapsing and remitting focal myositis with fasciitis].
は じめに 限局性筋炎(focal myositis: FM)は 四肢, 体幹 における限局性の痛み と腫脹 などの症状 に て発症 し,同 部の生検 な どで診 断 される1~3). 今 回我々は,画 像所見 と生検 にて筋膜 に炎症所 見 を伴 う限局性筋炎の1例 を経験 したので報告 す る. 症 例 患者:28歳,女 性.主 訴:右 下腿部痛,発 熱. 現病 歴:1996年8月 よ り両大腿 部の痛み と発熱 が 出現 したため近 医を受診 した.CK 986IU/l, Ald 10.3mIU/ml,CRP 13.7mg/dlよ り筋炎の疑 いで入院 となった.入 院後,症 状 は自然軽快 し, 検査所見 も正常 とな り退 院した.退 院後 は月1 回程度,大 腿部に限局 した腫 脹 と痛みが出現 し たが,自 然消失す るため経過観察中であった. 1999年8月10日 よ...
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Acquired Amegakaryocytic Thrombocytopenic Purpura (AATP) is a rare cause of thrombocytopenia presenting over a wide age group with symptoms of bleeding and bone marrow showing isolated absence of megakaryocytes in an otherwise normal marrow. Here, we report a case of AATP in a three year old female child who was then treated with anti thymocyte globulin successfully. We report this case because...
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The possible pathogenetic mechanisms responsible for the production of acquired amegakaryocytic thrombocytopenic purpura (AATP) were investigated in a group of patients with this disorder. Absence of megakaryocytes and small platelet glycoprotein-bearing mononuclear cells, as determined by immunochemical staining of patient marrows with an antisera to platelet glycoproteins, suggested that the ...
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Acquired amegakaryocytic thrombocytopaenic purpura (AATP) is a rare haematological condition characterised by isolated thrombocytopaenia with normal other cell lines. It is often initially misdiagnosed as immune thrombocytopaenic purpura but has characteristic bone marrow findings of reduced megakaryocyte numbers. The optimal treatment of AATP is not clearly defined but revolves around immunosu...
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ژورنال
عنوان ژورنال: American Journal of Hematology
سال: 2004
ISSN: 0361-8609,1096-8652
DOI: 10.1002/ajh.10475